Answer
Avalglucosidase alfa (Nexviadyme) is administered by intravenous infusion under an experienced physician’s supervision, starting at 1 mg/kg/hour and increasing gradually every 30 minutes according to response and comfort if no infusion-associated reactions occur, with vital signs checked before each increase.
Sources for this answer
- Nexviadyme 100 mg powder for concentrate for solution for infusionSANOFI · emc · SmPC §4.2 Posology and method of administration · Version 4Document updated
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