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Dermatomyositis — RCPSC IM MCQ

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HardRheumatologyDermatomyositisRCPSC IM

A 53-year-old has dermatomyositis with dysphagia and anti-TIF1-gamma antibodies. Which additional action is particularly important?

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Correct answer: CUndertake age-indicated and risk-directed malignancy evaluation

The best answer is “Undertake age-indicated and risk-directed malignancy evaluation”. Dermatomyositis, especially with anti-TIF1-gamma, carries increased malignancy risk. Screening is individualized by age, phenotype and antibody profile while muscle and swallowing disease is treated. Dysphagia also requires urgent aspiration-risk assessment because respiratory and swallowing complications can become more immediate than muscle weakness.

Reference: Canadian Rheumatology Association, clinical guidelines: https://rheum.ca/resources/publications/