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Aplasia Cutis Congenita — SCE Dermatology MCQ

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HardPaediatric DermatologyAplasia Cutis CongenitaSCE Dermatology

A newborn has a 6 cm membranous vertex scalp defect with visible pulsation and dilated surrounding veins. Before operative repair, which investigation is most important?

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Correct answer: EMRI with venous sinus imaging

A large midline membranous aplasia cutis defect can overlie a skull defect or communicate with the superior sagittal sinus. Cross-sectional imaging with venous assessment is required before biopsy, debridement or reconstruction because uncontrolled sinus haemorrhage can be catastrophic.

Reference: https://academic.oup.com/bjd/pages/bad-guidelines