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Sturge-Weber Syndrome — SCE Dermatology MCQ

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HardPaediatric DermatologySturge-Weber SyndromeSCE Dermatology

A newborn has a unilateral capillary malformation involving the forehead and upper eyelid. Neurological examination is normal and no seizures have occurred. Which action is most appropriate?

Educational content. Not a substitute for clinical judgement or local policy.

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Correct answer: B — Paediatric ophthalmology and neurology review through the vascular-birthmark pathway

Explanation lettering: E = shown as C · C = shown as D · D = shown as E

B is correct. A port-wine stain involving the forehead or eyelid carries clinically important ocular and neurological associations. Glaucoma may be present without obvious symptoms, and a normal neonatal neurological examination does not exclude Sturge–Weber syndrome; prompt ophthalmology and coordinated paediatric specialist assessment are therefore appropriate. A addresses appearance but not organ risk. C delays detection of potentially sight-threatening glaucoma. D describes an unrelated tumour syndrome. E confuses a persistent capillary malformation with an infantile haemangioma and assigns a diagnosis without the required phenotype or assessment.

Reference: BAD vascular birthmarks information: https://www.bad.org.uk/pils/vascular-birthmarks