Answer
Protein breakdown produces nitrogen. The diet limits nitrogen production while sodium phenylbutyrate provides another route for removing it; the diet must remain nutritionally adequate and specialist-managed.
Sources for this answer
- PHEBURANE 350 mg/mL oral solution — Current selected SmPCemc · Summary of Product Characteristics
- Ammonaps 500 mg tablets — Current selected SmPCemc · Summary of Product Characteristics