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Idiopathic pulmonary fibrosis — RACP Written MCQ

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EasyRespiratoryIdiopathic pulmonary fibrosisRACP Written

A 72-year-old man has progressive exertional dyspnoea and dry cough. Examination reveals fine bibasal inspiratory crackles and clubbing. HRCT shows basal subpleural reticulation, honeycombing and traction bronchiectasis without ground-glass predominance. What is the most likely diagnosis?

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Correct answer: EIdiopathic pulmonary fibrosis

Basal subpleural honeycombing and traction bronchiectasis with dry cough and clubbing are typical of usual interstitial pneumonia, most commonly idiopathic pulmonary fibrosis.

Reference: Australian Asthma Handbook; TSANZ guidance; Therapeutic Guidelines: Respiratory