ADPKD — RACP Paediatrics MCQ

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A 14-year-old has hypertension and bilateral renal cysts. Father and grandmother had cyst surgery. No hepatic fibrosis. What is the diagnosis?

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Correct answer: C — ADPKD

Bilateral cysts with AD family history, no hepatic fibrosis = ADPKD (PKD1/PKD2). Rarely causes ESKD in childhood. Long-term monitoring needed.

Reference: RACP Paediatric Curriculum – Nephrology/Genetics