Moyamoya disease — RACP Paediatrics MCQ

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HardNeurologyMoyamoya diseaseRACP Paediatrics

A 6-year-old has recurrent TIAs. Angiography shows bilateral ICA stenosis with 'puff of smoke' collateral network. What is the diagnosis?

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Correct answer: A — Moyamoya disease

Bilateral ICA stenosis/occlusion with moyamoya collaterals. Associated with Down syndrome, NF1, SCD. Surgical revascularisation reduces stroke risk.

Reference: RCH Melbourne – 2023 – Stroke CPG