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ILD – dermatomyositis — RACP Paediatrics MCQ

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HardRespiratoryILD – dermatomyositisRACP Paediatrics

A 10-year-old with dermatomyositis develops progressive dyspnoea. HRCT shows ground-glass opacities. Anti-MDA5 is positive. What is the most likely complication?

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Correct answer: BInterstitial lung disease

ILD associated with anti-MDA5 antibody dermatomyositis can be rapidly progressive. Treatment is aggressive immunosuppression.

Reference: RACP Paediatric Curriculum – Respiratory/Rheumatology