skip to main content

HCM – IDM — RACP Paediatrics MCQ

Instant feedback + full explanation. One question, done properly.

ModerateCardiologyHCM – IDMRACP Paediatrics

A 6-month-old infant of a diabetic mother presents with severe heart failure. Echocardiogram shows marked septal hypertrophy causing LVOT obstruction. There is no family history of cardiac disease. What is the most likely diagnosis?

Educational content. Not a substitute for clinical judgement or local policy.

Reveal the answer and explanation

Correct answer: D — Hypertrophic cardiomyopathy

Hypertrophic cardiomyopathy in infants of diabetic mothers (IDMs) is caused by fetal hyperinsulinism leading to glycogen deposition and myocardial hypertrophy, particularly of the interventricular septum. It is usually transient and resolves within 2-4 months. Management is supportive; beta-blockers may be needed if there is significant LVOT obstruction. Inotropes should be avoided.

Reference: RCH Melbourne – 2023 – Cardiomyopathy CPG; RACP Paediatric Curriculum – Cardiology