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Henoch-Schönlein purpura — RACP Paediatrics MCQ

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ModerateGIHenoch-Schönlein purpuraRACP Paediatrics

A 6-year-old presents with colicky abdominal pain, a palpable purpuric rash over the buttocks and lower limbs, and swollen ankles. Urine dipstick shows 2+ blood and 1+ protein. What is the most likely diagnosis?

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Correct answer: AHenoch-Schönlein purpura

The classic tetrad of IgA vasculitis (Henoch-Schönlein purpura) includes palpable purpura (mandatory criterion), arthritis/arthralgia, abdominal pain, and renal involvement (haematuria/proteinuria). Abdominal pain occurs in ~60% and can precede the rash. Intussusception is a recognised complication.

Reference: RCH Melbourne – 2023 – Henoch-Schönlein Purpura CPG; RACP Paediatric Curriculum – Rheumatology