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G6PD Fava Beans Crisis — RACP Paediatrics MCQ

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ModerateHaematology & OncologyG6PD Fava Beans CrisisRACP Paediatrics

Mediterranean child: jaundice, dark urine after fava beans. Hb dropped, bite cells, Heinz bodies. Diagnosis?

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Correct answer: EG6PD deficiency

Oxidative stress → acute haemolysis. G6PD may be falsely normal during crisis (retest 3 months).

Reference: RCH Melbourne – 2024