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Incomplete Kawasaki Disease — RACP Paediatrics MCQ

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ModerateInfectious DiseaseIncomplete Kawasaki DiseaseRACP Paediatrics

A 2-year-old presents with high fever for 7 days, rash, conjunctivitis, and lip cracking. He meets 3 of 5 classic Kawasaki criteria. CRP is 85 mg/L. Echo shows a coronary Z-score of 2.8. What is the diagnosis?

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Correct answer: CIncomplete Kawasaki disease (meeting criteria by supplemental lab/echo findings)

Incomplete KD: fever ≥5 days + 2-3 classic criteria. If CRP ≥30 and supplemental criteria are met (echo abnormalities, lab findings such as elevated ESR/CRP, anaemia, thrombocytosis, hypoalbuminaemia, pyuria), treatment with IVIG should be given. Coronary Z-score ≥2.5 supports the diagnosis.

Reference: RCH Melbourne – 2024 – Clinical Practice Guidelines: Kawasaki Disease