Juvenile Dermatomyositis Presentation — RACP Paediatrics MCQ

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ModerateNeurology & DevelopmentJuvenile Dermatomyositis PresentationRACP Paediatrics

A 15-year-old girl presents with progressive proximal muscle weakness, myalgia, and a heliotrope rash around the eyes and Gottron papules on the knuckles. Creatine kinase is markedly elevated. What is the diagnosis?

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Correct answer: A — Juvenile dermatomyositis

JDM presents with proximal weakness, characteristic rash (heliotrope, Gottron papules), and elevated CK. Muscle biopsy shows perivascular inflammation. MRI shows muscle oedema. Treatment includes corticosteroids and methotrexate. Calcinosis is a significant long-term complication.

Reference: RCH Melbourne – 2024 – Clinical Practice Guidelines: Juvenile Dermatomyositis