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Critical Coarctation with Duct Closure — RACP Paediatrics MCQ

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EasyCardiologyCritical Coarctation with Duct ClosureRACP Paediatrics

A 2-day-old neonate has severe metabolic acidosis, poor perfusion, and absent femoral pulses. Echocardiogram shows a severely hypoplastic aortic arch with a closing ductus arteriosus. What is the most critical intervention?

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Correct answer: BProstaglandin E1 infusion

Interrupted aortic arch or critical coarctation with duct-dependent systemic circulation requires urgent PGE1 to reopen the ductus arteriosus and restore systemic perfusion. This is lifesaving and must not be delayed.

Reference: RCH Melbourne – 2024 – Clinical Practice Guidelines: Duct-Dependent CHD