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Acute Splenic Sequestration — RACP Paediatrics MCQ

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HardHaematology & OncologyAcute Splenic SequestrationRACP Paediatrics

A 10-year-old with SCD presents with sudden pallor, tachycardia, rapidly enlarging spleen. Hb drops from 80 to 40. Reticulocytes elevated. Diagnosis?

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Correct answer: BAcute splenic sequestration

Acute splenic sequestration: sudden trapping of RBCs in spleen, acute anaemia, splenomegaly.

Reference: RCH Melbourne – 2024 – Clinical Practice Guidelines: SCD