Hirschsprung Disease — RACP Paediatrics MCQ
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Correct answer: D — Give fluids, antibiotics and rectal washouts with surgical consultation
Explanation lettering: C = shown as B · D = shown as C · B = shown as D
B is correct. The presentation is Hirschsprung-associated enterocolitis, which requires urgent resuscitation, broad antimicrobial treatment, rectal washouts/decompression and paediatric surgical involvement. A under-treats a potentially fatal complication. C bowel preparation and colonoscopy risk deterioration and delay treatment. D antimotility therapy worsens obstruction. E enteral feeding is inappropriate during acute distension and systemic illness.
Reference: RCH Melbourne, Hirschsprung-associated enterocolitis: https://www.rch.org.au/clinicalguide/guideline_index/Hirschsprung_associated_enterocolitis_HAEC/