skip to main content

Cystic Fibrosis — RACP Paediatrics MCQ

Instant feedback + full explanation. One question, done properly.

HardRespiratoryCystic FibrosisRACP Paediatrics

A 15-year-old boy with cystic fibrosis cultures Burkholderia cepacia complex from sputum for the first time. His FEV1 is 45% predicted. What is the clinical significance?

Educational content. Not a substitute for clinical judgement or local policy.

Reveal the answer and explanation

Correct answer: D — It is associated with accelerated lung decline, may cause cepacia syndrome, and has infection control implications

BCC in CF is associated with accelerated lung decline, risk of cepacia syndrome, and is a relative contraindication to lung transplantation. It requires strict segregation from other CF patients.

Reference: Australian Cystic Fibrosis Guidelines – 2024 – Infection Control in Cystic Fibrosis