Myotonic Dystrophy Anaesthetic Management — FRCA Final MCQ

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HardGeneral AnaesthesiaMyotonic Dystrophy Anaesthetic ManagementFRCA Final

A 33-year-old woman with myotonic dystrophy type 1 requires GA for laparoscopic ovarian cystectomy. Which statement is correct?

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Correct answer: D — Volatile agents may trigger myotonic contractions

Volatiles and suxamethonium trigger myotonic contractions in DM1. Suxamethonium causes sustained intractable contracture unresponsive to NdNMBAs or dantrolene. Neostigmine worsens myotonia — sugammadex preferred. TIVA avoids volatile-triggered myotonia. Very high post-op respiratory failure risk.

Reference: RCOA – 2024 – Anaesthetic management of myotonic dystrophy