Cystic Fibrosis
Overview and management of CF.
Reviewed by Dr Kola Tytler MBBS CertHE MBA MRCGP (General Practitioner)
Last reviewed: 21 October 2025
Clinical Guidelines
ECFS Guidelines Archive
National
NICE guideline [NG78]National
NICE guideline [NG78]: Cystic fibrosis: diagnosis and managementNational
Clinical care guidelines for cystic fibrosis-related diabetes: a position statement of the American Diabetes Association and a clinical practice guideline of the Cystic Fibrosis FoundationLocal
Cystic Fibrosis Foundation Clinical Care GuidelinesLocal
Cystic Fibrosis Foundation consensus guidelines for the care of individuals with advanced cystic fibrosis lung diseaseLocal
Cystic Fibrosis Foundation Evidence-Based Guideline for the Management of Infants with Cystic FibrosisLocal
Cystic Fibrosis Pulmonary Guidelines: Chronic Medications for Maintenance of Lung HealthLocal
Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis FoundationLocal
ECFS best practice guidelines: the 2018 revisionLocal
Guidelines for UK clinical psychology services in cystic fibrosis (2024)Local
Infection Prevention and Control Guideline for Cystic Fibrosis: 2013 UpdateLocal
ISPAD Clinical Practice Consensus Guidelines 2022: Management of cystic fibrosis-related diabetes in children and adolescentsLocal
NICE guideline [NG78]: Cystic fibrosis: diagnosis and managementLocal
US Cystic Fibrosis Foundation and European Cystic Fibrosis Society consensus recommendations for the management of cystic fibrosisLocal