Answer
Cystagon (mercaptamine bitartrate) reduces cystine accumulation by reacting with cystine to form a mixed disulfide of cysteamine and cysteine, which is exported from lysosomes by an intact lysine transport system.
Sources for this answer
- Cystagon 50 mg hard capsulesRecordati Rare Diseases UK Ltd · emc · SmPC §5.1 Pharmacodynamic properties · Version 10Document updated
Sources checked