How can I differentiate Waldenström's Macroglobulinaemia from other causes of elevated IgM levels in a patient?

Guideline-aligned answer with reasoning, red flags and references. Clinically reviewed by Dr Kola Tytler MBBS CertHE MBA MRCGP.

Posted: 22 August 2025Updated: 22 August 2025 Guideline-Aligned (High Confidence) Clinically Reviewed
Dr Kola Tytler MBBS CertHE MBA MRCGPClinical Lead • iatroX

To differentiate Waldenström's macroglobulinaemia (WM) from other causes of elevated immunoglobulin M (IgM) levels, a combination of clinical, laboratory, and pathological assessments is essential.

Firstly, WM is characterised by a monoclonal IgM paraprotein detected on serum protein electrophoresis and immunofixation, whereas polyclonal IgM elevation suggests reactive or inflammatory causes rather than WM .

Secondly, bone marrow biopsy in WM shows infiltration by lymphoplasmacytic lymphoma cells, which is a key diagnostic feature distinguishing it from other IgM elevations such as those seen in chronic infections or autoimmune diseases .

Thirdly, the presence of symptoms related to hyperviscosity, anaemia, or organomegaly supports WM diagnosis over benign IgM elevations .

Additionally, molecular testing for the MYD88 L265P mutation, present in over 90% of WM cases, provides a highly specific marker to differentiate WM from other IgM-secreting disorders .

Finally, other causes of elevated IgM such as IgM monoclonal gammopathy of undetermined significance (MGUS) or other B-cell lymphoproliferative disorders require exclusion through comprehensive clinical and pathological evaluation ; .

Educational content only. Always verify information and use clinical judgement.

How can I differentiate Waldenström's Macroglobulinaemia from other ca