How should I manage a patient with congenital heart disease who presents with respiratory distress?

Guideline-aligned answer with reasoning, red flags and references. Clinically reviewed by Dr Kola Tytler MBBS CertHE MBA MRCGP.

Posted: 16 August 2025Updated: 16 August 2025 Guideline-Aligned (High Confidence) Clinically Reviewed
Dr Kola Tytler MBBS CertHE MBA MRCGPClinical Lead • iatroX

When a patient with congenital heart disease presents with respiratory distress, it is crucial to recognise this as a potentially serious complication requiring urgent assessment , . Respiratory distress can be a sign of decompensation in patients with congenital heart disease , . The immediate priority for an Admin is to ensure the patient receives prompt clinical review by a General Practitioner or is referred urgently to secondary care, such as an Emergency Department, depending on the severity of their symptoms .

  • Assess urgency: Respiratory distress, or breathlessness, should be assessed for severity, considering factors such as the patient's work of breathing, oxygen saturation if available, and overall clinical appearance . For children, signs like increased respiratory rate, nasal flaring, or intercostal recession indicate significant distress , .
  • Facilitate clinical review: Ensure the patient is seen by a clinician as soon as possible . This may involve arranging an urgent same-day appointment or advising attendance at an urgent care centre or Emergency Department .
  • Communicate key information: When referring or handing over, clearly state that the patient has congenital heart disease and is presenting with respiratory distress, as this background is critical for clinical decision-making .

Managing complications in patients with congenital heart disease often requires specialist input, highlighting the importance of timely referral to appropriate medical services .

Educational content only. Always verify information and use clinical judgement.